ERT 2013

Monitoring hillslope moisture dynamics with surface ERT

Hillslopes are one of the basic units that mainly control water movement and flow pathways within catchments. The structure of their shallow subsurface affects water balance , e.g. infiltration, retention, and runoff. Nevertheless, there is still a gap of knowledge of the hydrological dynamics on hillslopes, notably due to the lack of generaliza-5 tion and transferability. To improve the knowle...

Enzyme replacement therapy (ERT) in pompe disease

Pompe disease (OMIM 232300) is an AR glycogenosis due to deficiency of the lysosomal enzyme alpha-glucosidase (GAA). As a result, glycogen storage occurs in muscles and patients present a wide clinical spectrum ranging from early onset severe cardiomyopathy (EOPD) to adult onset forms (LOPD). Severe loss of GAA activity correlates with early onset and severe phenotypes. Residual enzyme activity...

S3.1 Are there ERT defined guidelines for Pompe disease?

disease confirmed by a biochemical and molecular genetic examinations (1). So far, ERT has been generally prescribed to patients with motor symptoms (muscle weakness) and/or respiratory involvement. Exclusion criteria encompassed a severe associated illness which would be expected to greatly shorten life expectancy. Alglucosidase (Myozyme) is administered biweekly i.v. as 20 mg/kg. Although the...

Design of high-speed ECT and ERT system

Ert Syste Ntroduction Problem Description Why Use Al?

This paper describes a tool to diagnose the cause of failure of a HP computer server. We do this by analyzing the dump of Processor Internal Memory (PIM) and maximizing the leverage of expert learning from one hardware failure situation to another. The tool is a rule-based expert system, with some nested rules which translate to decision trees. The rules were implemented using a metalanguage wh...